Porphyria Cutanea Tarda

cutanea tarda = chronic skin condition

 

 

Porphyria Medical Guide

 

Porphyria Cutanea Tarda

The most common subtype of porphyria, this disorder results from a deficiency of uroporphyrinogen decarboxylase (UROD), an enzyme critical to the sythesis of heme, an important consituent in hemoglobin, the molecule responsible for carrying oxygen throughout the bloodstream.

Those with porphyria cutanea tarda (PCT) are advised to...
• stay out of the sun, especially during the summer (due to photosensitivities that can lead to blisters and skin erosions on exposed areas)
• abstain from alcohol consumption
• skip iron supplements (PDF: Iron Overload In Porphyria Cutanea Tarda)
• avoid estrogenic compounds and chlorinated cyclic hydrocarbons

Genetics: Eighty percent of porphyria cutanea tarda cases do not present with an inherited UROD gene mutation and are classified as sporadic. Of the remaining (inherited) cases, 20% were passed via an autosomal dominant pattern.

Patient's Sourcebook On Porphyria

Since many with porphyria's also experience exacerbation of symptoms when eating gluten-containing foods, you may want to consider enjoying gluten-free "pasta" such as those available at CalorieFreeNoodles.com

 

Calorie Free Noodles